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SKU: 144-65959-100-RB

Anti-HEXA Antibody

Blue Ice

Specifications

Specification Details
Species Reactivity Human, Mouse
Application WB
Label Unconjugated
Gene ID 3073
Accession No. P06865
Background This gene encodes a member of the glycosyl hydrolase 2 family of proteins. The encoded preproprotein is proteolytically processed to generate the alpha subunit of the lysosomal enzyme beta-hexosaminidase. This enzyme, together with the cofactor GM2 activator protein, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Mutations in this gene lead to an accumulation of GM2 ganglioside in neurons, the underlying cause of neurodegenerative disorders termed the GM2 gangliosidoses, including Tay-Sachs disease (GM2-gangliosidosis type I). Alternative splicing results in multiple transcript variants, at least one of which encodes a preproprotein that is proteolytically processed.
Primary / Secondary Primary Antibody
Isotype IgG
Buffer PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
Clonality Polyclonal
Host Rabbit
Catalog Number
144-65959-100-RB
Name
Anti-HEXA Antibody
Price(100 ul)
Pack Size
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